Rhabdomyosarcoma is a malignant
neoplasm of primitive mesenchyme exhibiting skeletal muscle differentiation.
Rhabdomyosarcoma, which can histo pathologically be of embryonal, alveolar,
botryoid and pleomorphic types; is a rare tumor in children, with an annual
incidence of 4.3 cases per million. Pleomorphic rhabdomyosarcomas is a rare
variant, occurring more commonly in adults.
We report a rare case of ocular
pleomorphic rhabdomyosarcoma in an 18-month-old child with atypical
presentation mimicking orbital cellulitis. A provisional diagnosis of orbital cellulitis was made based on clinical and radio logical examination and was planned for surgery. Histopathology confirmed the diagnosis of pleomorphic
rhabdomyosarcoma. This case shows that pleomorphic rhabdomyosarcoma may also
occur in children, it may mimic symptoms of orbital cellulitis, and any fast
growing swelling should be carefully examined with a high degree of suspicion
of this entity.
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